Unilateral Pulmonary Fibrosis with Pulmonary Artery Agenesis (PAA): A Case Report
DOI:
https://doi.org/10.12974/2312-5470.2022.08.01Keywords:
Interstitial lung disease, Unilateral pulmonary fibrosis, Pulmonary artery agenesisAbstract
Unilateral pulmonary artery agenesis (AUAP) is a rare clinical condition that can be seen either in isolation or in combination with other congenital vascular disorders. When isolated, the patient may be almost asymptomatic and only become aware of this anomaly through medical examinations performed for other reasons.
Here we discuss the case of a female patient with chest CT evidence of unilateral fibrous thickening, with pulmonary hypoexpansion; investigations revealed the coexistence of AUAP.
This clinical association is described by very rare case-reports in the literature.
References
Lesnyak VN, Danilevskaya OV, Averyanov AV. Unilateral Pulmonary Fibrosis and Systemic Sclerosis. ATS Journal Vol. 190, Issue 9. https://doi.org/10.1164/rccm.201407-1253IM
Kimura T, Mizutani T. Unilateral pulmonary fibrosis following ipsilateral single-lung ventilation and anesthesia. Masui 2001; 50: 651-654.
Sakai S, Murayama S, Soeda H, et al. Unilateral proximal interruption of the pulmonary artery in adults: CT findings in eight patients. J Comput Assist Tomogr 2002; 26: 777-783. https://doi.org/10.1097/00004728-200209000-00019
Adnan K, Sana K, Zafar R, et al. An interesting case of unilateral pulmonary fibrosis. Chest J 2019; 156 (4 Supplement A1830). https://doi.org/10.1016/j.chest.2019.08.1585