Congenital Left Upper Lobe Agenesis: Report of a Case
DOI:
https://doi.org/10.12974/2312-5470.2014.01.02.2Keywords:
Agenesis, Bronchiectasis, Lobar, Pulmonary.Abstract
Lobar agenesis is an extremely rare condition which is characterized by the absence of the lobar pulmonary artery, pulmonary vein, bronchi and parenchyma. Most frequently the affected lobe is the left upper lobe, and patients usually survive to older ages. In the report below we present a case of the left upper lobe agenesis and bronchiectasis of the superior segment of the ipsilateral lower lobe. The thoracic computed tomography scan and fiberoptic bronchoscopy are important diagnostic tools. The patient remained problem-free after the segmentectomy of the bronchiectatic parenchyma.
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